Especially dangerous congenital disease Sprengel

Sprengel disease - is a congenital disease of , which appears in cases of intrauterine growth disorders of the fetus.

This violation leads to a significant deterioration in the quality of life and requires surgical intervention.

Therefore, if a symptom of a disease is found, you should immediately get medical advice.

. What are the features of the

pathology? Congenital disorder, which manifests itself in the form of a high standing blade. Pathology develops during the intrauterine period.

In the normal state, the scapula is formed with a shoulder girdle. At first it is high enough, but then falls to the usual place.

If certain factors impede the normal development process, the blade remains in the wrong position.

It should be borne in mind that this violation is often combined with other defects:

• by the appearance of additional semi-vertebrae;
• with the Klippel-Feil syndrome;
• by rib fusion;
• to the club foot.

The disease can affect one scapula or two at a time. However, bilateral defeat is much less common. In this case, the scapula is localized unevenly - usually the left is higher than the right one.

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The causes of pathology are found in the mother

The main cause of the development of Sprengel's disease in children is the effect of harmful factors on the body of a pregnant woman.

They can be external or internal and affect the development of the child during the laying of the upper shoulder girdle and spine.

Most often the disease is the result of such factors:

• abnormal position of the embryo in the uterus;
• complicated pregnancy;
• compression of the fetus wall of the uterus.

The high position of the scapula is often combined with other disorders of the spine.

Classification of

There are two main forms of this disease - muscular and bony. In medical practice, muscle strain is not so severe. It is characterized by hypotrophy of the shoulder muscles.

The difference in the arrangement of the scapula in height is usually about 5-12 cm. At that, the joint of the shoulder is shifted forward and rises. This condition is characterized by such abnormalities as difficulty in bending and retracting the arm.

Bone disorder is that the upper part of the scapula reaches the occiput. In this type of disease between the spinal column and the shovel, an omvertebral bone is formed - it completely immobilizes the scapula.

Symptoms are visible to the naked eye

This pathology can be seen immediately by the anomalous arrangement of the scapula. In addition, her symptoms include loss of mobility of the shoulder and arm. Sometimes the disease can provoke the onset of pain syndrome.

In simple cases, a person is only concerned about a cosmetic disorder. In more complex cases, the scapula is too high in relation to the thorax and looks much smaller. It strongly deforms, and its end can reach the back of the head.

In addition to deformation, atrophy of rhomboid and trapezius muscles develops. Also, the doctor during the examination can reveal an additional bone, which is located along the vertebral margin of the scapula.

Children often have a fibrous cord between the tip of the scapula and the cervical vertebrae. The person experiences difficulties with the vertical lead of the hand.

Statement of diagnosis

In the photo, a person with asthma

has to undergo an external examination and make a radiograph in order to make the correct diagnosis.

With this study, a connection can be found between the cervical spine and the scapula, which is partial or complete.

This compound resembles a narrow bone strip and binds to the scapula and spine with a cartilaginous tissue.

Objectives and methods of treatment

The main task of conservative therapy is to strengthen the muscular tissue of the shoulder and chest. It is also used to increase motor activity and prevent secondary deformations.

Usually, such treatment is used at the initial stages of Sprengel's disease and consists of performing massage, swimming and physical therapy.

Very useful applications with paraffin and ozocerite on the affected areas.

It should be understood that spontaneous improvement of the patient's condition with this disease is impossible.

If a child aged 8-14 years with a congenital disease has a slight restriction of motor activity and a minor cosmetic defect, no surgical intervention is performed.

In such a situation, children should be engaged in therapeutic gymnastics, which will help to adjust the work of the shoulder girdle.

Surgery

Up to 8 years, the indications for surgical intervention are much wider, because as the body grows, deformation can increase. In addition, there is a risk of secondary deformations of the shoulder girdle.

If there are serious disorders and severe deformation of the muscular and bone tissue, an operation is indicated.

During this procedure, the blade is mobilized, after which it is fixed in the right place. The earlier the child will be made such an operation, the better the results will be achieved in the future.

It should be noted that it is impossible to completely correct the existing deformation. In neglected cases, excessive attempts to move the scapula to a normal level can provoke dangerous complications.

Therefore, the only way to treat with moderate to severe deformity is surgery.

Preventive measures

After the operation for one and a half years, you need to practice therapeutic gymnastics. Preventing relapses is in swimming or volleyball.

Massage and gymnastics are indicated for children and before surgery. These measures help to strengthen the muscle tissue of the back and form a correct posture.

They also help prevent the progression of existing scoliosis or other deformities.

Therapeutic exercise is of great importance for the therapy of this disease.

People with the pathology of Sprengel need to perform general developmental exercises that help restore adaptation to physical exertion, increase muscle endurance.

The course of correctly selected gymnastics helps to achieve positive results after 1-2 years.

Disease - a latent danger to the entire body

The main complication of pathology is that when it develops a person can not take his hand vertically. The abduction is carried out until the shoulder reaches the shoulder blade. The greater the angle of its turn, the smaller the arm's distance.

Operations to correct this disorder can also lead to serious complications, the main one of which are paresis of the brachial plexus. Similar problems arise in about every tenth case.

Sprengel's disease - is quite a dangerous disorder, which can lead to extremely negative health consequences for .To prevent this from happening, you need to start treating the disease as soon as possible. Therefore, when identifying the symptoms of a disease, you should immediately contact an experienced doctor.