Shay-Drageer's syndrome is very similar to Parkinson's, otherwise called idiopathic orthostatic hypotension.
It is a variant of multisystem atrophy with predominant vegetative failure.
Violations of the functions of the nervous system lead to an imbalance of all organs that it controls. This affects the heart rate, blood pressure, glandular secretion, and focus.
In the event of Shay-Draeger, many parts of the nervous system degenerate.
Contents
- Causes of
- Causes of
- Symptoms of
- Syndrome Diagnostic approach
- Treatment of
- patients Objectives of
- Methods used
- Complications arising during treatment
- Forecast disappointing
Causes of occurrence of
Causes of the onset of the disease and its nature have not yet been elucidated, it is possible.they have genetic roots. Most often men suffer from 40 to 60 years.
Sometimes, the disease can be triggered by taking certain medications.
These include:
- diuretics, removing excess water from the body, resulting in a drop in blood pressure;
- preparations used for vasodilation;
- substances that reduce blood pressure.
Today you can only talk directly about the causes of loss of consciousness, it is:
- heart rhythm disturbance;
- discrepancy between cardiac output and myocardial support;
- decrease in blood circulation is associated with a decrease in the amount of recurrent to the heart of blood;
- disruption of the distribution function of reduced blood volume;
- heart failure.
Symptoms of
Syndrome The first sign may be an inability to achieve an erection( impotence) and lack of sexual desire. 
Both men and women with Shia-Dryger syndrome have major problems with urination.
Most often this is due to low urethral pressure.
Patients noted a decrease in the number of tears and saliva, a sharp drop in blood pressure when you get up, significantly reduces the amount of sweat, constipation. Violation of motor functions and coordination of movements occurs according to the type of Parkinson's disease.
Patients appear unstable gait, they complain of rapid fatigue. Due to constant dizziness a person can not stand for a long time, his eyes darken and his vision is disturbed.
Sensation of a near fain pursues a sick person permanently.
The more the disease progresses, the worse the patient becomes.
In a more severe clinical picture, syncope occurs directly in bed when sitting. When the patient is forcibly transferred to a vertical position, deep fainting and cerebral ischemia occur.
In most cases, after the onset of hemodynamic disorders, muscle tremors appear. Expressed manifestations of Parkinson's disease are observed in 60% of patients.
Trembling of limbs, monotonous voice is manifested in 1/3 patients. Dysfunction of the swallowing function, sucking reflex appears somewhat less often.
40% of patients develop an atactic gait. It is characterized by excessive lifting of widely spaced legs. This is due to the destruction of the functions of the cerebellum.
In what cases can the appearance of the syndrome be suspected:
- impaired coordination of movements, gait;
- fast fatigue;
- tremor of the extremities;
- frequent dizziness and pre-stupor states that occur with a sharp rise;
- dry mouth, disorders of urogenital function( urinary incontinence), impotence in men and lack of libido in women;
- frequent constipation;
- hot flashes or a feeling of chilliness at normal air temperature;
- very loud snoring;
- throat paralysis;
- double vision.
Because Shay-Draeger syndrome has many primary symptoms, their combinations can be very diverse.
Diagnostic approach
If the doctor has information about the nature of the syndrome, then it will not be difficult for him to diagnose at the early stages of the manifestation of the disease.
The patient should be hospitalized in a hospital to exclude Parkinson's disease and the effects of encephalitis.
Vegetative disorders that occur in the syndrome( rectum atony, enuresis, anhidrosis) appear much earlier than in parkinsonism and are more pronounced.
The decisive factor in diagnosis is the study of the patient's anamnesis and lifestyle. Some clarity can make conversation with the patient's relatives.
As a result, the following issues are clarified:
- pronounced arterial hypotension;
- impossibility of long standing or abrupt rising;
- permanent fainting.
For the diagnosis use a rotary table, on which the patient for some time is in a horizontal position.
Then the table is sharply turned to the vertical position, as a result of which the patient's pressure drops sharply.
Treatment of patients
The use of complex treatment( ephedrine, nialamide, pindolol, obmedan indomethacin, neurukal), is associated with the risk of arterial hypertension.
Therefore, drugs should be administered with extreme caution.
Objectives of
Treatment of Shay Dreiger syndrome is aimed primarily at increasing blood pressure and leveling the most pronounced symptoms that make a person disabled.
Methods used
One of the methods of therapy is to limit the amount of space that can be filled with blood. To do this, apply tight bandage of the extremities and pelvic region.
The patient is wearing inflatable suits, specially designed for this. A good effect gives swimming.
The second method is aimed at increasing blood pressure, by increasing the amount of blood. In this case, complex therapy is prescribed.
The patient should fully eat, shows a salt-rich diet, a plentiful drink. Human food should contain a large number of fibers of plant origin.
Reduces the amount of food with a high carbohydrate content. Practice is the introduction of drugs that promote salt retention in the body.
A positive result is the implantation of a pacemaker, which is able to set the heart rate to one hundred beats per minute.
During sleep, the patient's head should be in a raised position. The patient must be provided with regular follow-up.
In what cases is sensory aphasia manifested and a sign of which diseases it is. Why subarachnoid hemorrhage occurs in the brain and what are its serious consequences for the body.
Complications arising during treatment of
When hypertension is reached( even during a brief but dramatic decrease in blood pressure), the risk of cerebral ischemia is significantly increased.
Forecast disappointing
In most cases, the disease progresses strongly .Relative stabilization is fixed very rarely, but nevertheless, for 3-5 years it is possible.
In general, after the appearance of the first signs of the disease, the lethal outcome occurs within 7-8 years.
The disease is quite rare, it is observed once for twenty thousand people. More than half of the cases occur in males.
Nevertheless, no one is insured from it. Therefore, you can not neglect the appearance of the slightest of its symptoms, but you should immediately seek professional help from specialists.
They will help dispel your fears if the diagnosis is not confirmed. Or, in a timely manner, prescribe a treatment if the syndrome does take place.
